The most common cause of restrictive cardiomyopathy is amyloidosis.
Amyloid deposits in the myocardium cause abnormal diastolic function with biatrial enlargement, concentric thickening of the left ventricle and reduced systolic function of usually both ventricles.
Cardiac involvement in systemic amyloidosis occurs in up to 50% and has a poor prognosis with a median survival of 6 months.
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| the 4-chamber and short axis late enhancement images. There is circumferential subendocardial enhancement extending into the neighboring myocardium. |
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